• Target：
• CLN6

• Gene Name：
• CLN6

• Protein Name：
• Ceroid-lipofuscinosis neuronal protein 6

• Human Gene Id：
• 54982

• Human Swiss Prot No：
• Q9NWW5

• Immunogen：
• The antiserum was produced against synthesized peptide derived from human CLN6. AA range:221-270

• Specificity：
• CLN6 Polyclonal Antibody detects endogenous levels of CLN6 protein.

• Formulation：
• Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.

• Source：
• Polyclonal, Rabbit,IgG

• Dilution：
• WB 1:500 - 1:2000. IHC 1:100 - 1:300. ELISA: 1:40000.. IF 1:50-200

• Purification：
• The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

• Concentration：
• 1 mg/ml

• Storage Stability：
• -15°C to -25°C/1 year(Do not lower than -25°C)

• Other Name：
• CLN6;Ceroid-lipofuscinosis neuronal protein 6;Protein CLN6

• Observed Band(KD)：
• 40kD

• Background：
• This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. [provided by RefSeq, Oct 2008],

• Function：
• disease:Defects in CLN6 are the cause of variant late-onset infantile neuronal ceroid lipofuscinosis (vLINCL) [MIM:601780].,online information:Neural Ceroid Lipofuscinoses mutation db,

• Subcellular Location：
• Endoplasmic reticulum membrane ; Multi-pass membrane protein . Endoplasmic reticulum .

• Expression：
• Epithelium,Lung,Urinary bladder,

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